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Atypical subacute sclerosing panencephalitis: Case report

Abstract

Subacute sclerosing panencephalitis (SSPE) is a progressive inflammatory disorder of the central nervous system with both poor prognosis and high mortality. the disease has been related to a persistent and aberrant measles virus infection and no effective treatment has been available. We report a case of SSPE with atypical features including seizures at onset and a fulminant course in a 8 years-old boy who had been previously immunized against measles.Univ Fed Juiz de Fora, Univ Hosp, Dept Internal Med, Neurol Serv, Juiz de Fora, MG, BrazilUniv Fed Fluminense, Niteroi, RJ, BrazilUniv Fed Juiz de Fora, Juiz de Fora, MG, BrazilUniversidade Federal de São Paulo, São Paulo, BrazilUniv Fed Rio de Janeiro, Rio de Janeiro, BrazilUniv Fed Juiz de Fora, Univ Hosp, Dept Internal Med, Juiz de Fora, MG, BrazilUniversidade Federal de São Paulo, São Paulo, BrazilWeb of Scienc

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