We report a case of intrasellar craniopharyngioma in a 34 year-old woman who presented with progressive headache and diplopia. Computed tomographic and magnetic resonance images showed a heterogeneous tumor originating from the sphenoid bone with ethmoid sinus and sella turcica extension. A sublabial rhinoseptal transsphenoidal surgery was performed. Craniopharyngiomas with intrasellar development are very rare. Intrasellar craniopharyngioma is uncommon, thirty-five cases has been reported in literature. the embryology, clinical features and radiographic investigation of these tumors are discussed.Univ Caxias Sul, Fac Med, São Paulo, SP, BrazilUniversidade Federal de São Paulo, Ecola Paulista Med, São Paulo, SP, BrazilUFRGS, ISCMPA, FFCMPA, São Paulo, BrazilUniversidade Federal de São Paulo, Ecola Paulista Med, São Paulo, SP, BrazilWeb of Scienc
