Cutaneous lymphomas: proposal for new classification

Abstract

Dosedanje klasifikacije kožnih limfomov (npr. Kielska) so temeljile na njihovih histoloških značilnostih in niso razlikovale med primarnimi in sekundarnimi kožnimi limfomi, zaradi česar imajo majhno praktično vrednost. Nova klasifikacija kožnih limfomov zato temelji na kombinaciji kliničnih, histoloških, imunohistokemičnih in genetskih kriterijev in daje smernice za zdravljenje vsakega posameznega bolnika. Limfome razvršča najprej na T- in B-celične, nato pa glede na potek in prognozo na indolentno, intermediarno, agresivno ter provizorično skupino.The currently used classifications of cutaneous lymphomas, such as that of Kiel, are based on their histologic characteristic, not distinguishing betweenprimary and secondary cutaneous lymphomas. Therefore, their practical value is limited. The new classification combines clinical, histologic, immunohistochemical and genetic criteria which instruct the treatment of the individual patient. Lymphomas are divided into T and B-cell types, and to the respect of their evolution and prognosis the indolent, intermediate, agressiveand provisory group are defined

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