Lupus panniculitis (LP) is a rare condition that primarily affects adults and is even more uncommon in the pediatric population. This rarity, combined with variable clinical presentations and limited diagnostic approaches in children, often leads to its misdiagnosis or being overlooked. Recently, a case involving a six year's old boy demonstrated the importance of recognizing early skin manifestations and providing timely treatment. The child was presented with painful swelling in the right hand and erythematous plaques on the face and trunk. Although the autoimmune workup yielded weakly positive results, a skin biopsy was performed, which confirmed the diagnosis of LP. This case report serves to emphasize the significance of identifying early skin manifestations and the advancements in diagnostic methods that aid in accurate diagnosis
