Unilateral Optic Disc Edema in GFAP Autoantibody-Positive Astrocytopathy

Abstract

Glial fibrillary acidic protein (GFAP) autoantibody-positive astrocytopathy is a recently described rare autoimmune disorder that predominantly presents as a meningoencephalitis characterized by hallmark linear perivascular radial enhancement on brain MRI (1). Bilateral optic disc edema manifests in nearly one-third of patients in cohort studies for this disorder (2-3). Here, we introduce a case of unilateral optic disc edema in a patient with autoimmune GFAP astrocytopathy

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