Ependymomas are the most common glial tumors of conus medullaris, filum terminale and cauda equina.1 Ependymomas have also been reported in the extraspinal soft tissues of the sacral region, producing bone deformity and growing to great size.2 These extraspinal ependymal tumors are thought to be congenital in origin.1 We report a case of myxopapillary extradural ependymoma with extraspinal extension in presacral region in a 17 year old male presenting with weakness of the left lower limbs