A 26-year-old female, presented with discomfort and a lump in the left side of abdomen. Examination showed a non-tender cystic mass in the left lumbar region extending down to the pelvis, the lower limit being palpable through the left fornix. Investigations revealed a cystic mass extending from the left renal area to the pelvis and a non-visualized left kidney. Cystoscopy could not identify the left ureteric orifice. Surgical exploration showed a blind ending left ureter as a cystic mass, containing clear fluid capped by a hypoplastic left kidney. The mass extended from the left renal area to the pelvis. Left sided nephroureterectomy was performed
