Dermatomyositis is an autoimmune disease characterized by chronic inflammation of skin and muscle. Anti-melanoma differentiation-associated gene 5 (MDA5) associated dermatomyositis is a recently described variant that displays a unique dermatological phenotype consisting of punched-out cutaneous ulcers, palmar erythema, papules or blisters at typical sites of dermatomyositis. Moreover, anti-MDA5 associated dermatomyositis patients have an increased risk to develop a rapidly progressive interstitial lung disease with a potentially fatal course. Cutaneous ulcers are an important predictor for the development of interstitial lung disease. We report an illustrative case of anti-MDA5 associated dermatomyositis.</p
