Spencer S. Eccles Health Sciences Library, University of Utah
Abstract
Childhood primary angiitis of the CNS (cPACNS) is a rare cause of neurologic dysfunction in children. Diagnosis requires angiographic or pathologic evidence of vasculitis in the brain or spinal cord in the absence of systemic vasculitis and after exclusion of other causes of CNS dysfunction. Onset is usually insidious in angiography-negative cases. We present a case of angiography-negative PACNS causing rapid onset of CNS dysfunction mimicking meningoencepahlitis, whcih was successfully treated with immune suppression
