BACKGROUND
Synovial sarcoma (SS) is a rare type of soft tissue sarcoma that is
usually developed from areas where synovial tissue exists, especially at
the extremities. Nevertheless, several cases of retroperitoneal SS (RSS)
have been described. We herein report a case of RSS presented in our
institution.
CASE SUMMARY
A 69-year-old female patient was admitted with a large, palpable, firm
mass in the right abdominal space SS. Computerized tomography scan
depicted a concentric, sharply marinated retro-peritoneal lesion which
was displacing the right kidney and the lower edge of the liver.
Subsequently, the patient underwent surgical excision of the mass with
additional right nephrectomy and resection of the right adrenal gland
and a part of the diaphragm. The final histological diagnosis of the
tumour was grade II monophasic RSS.
CONCLUSION
RSS is encountered in the biphasic type, the monophasic fibrous, and the
monophasic epithelial category as well. Relevant clinical manifestations
are not always documented at early stages. Therefore, the final
diagnosis is posed after complete histological examination taking into
consideration the results of immunochemistry and genetic analysis.
Therapeutic approach happens often late when metastases at the lungs and
the liver are apparent. Thus, 5-year survival rates remain low