We herein present the case of a 70-year old lady with arrhythmogenic right ventricular cardiomyopathy (ARVC) and recurrent episodes of syncope. She was referred to our department due to an episode of sustained ventricular tachycardia (VT) which caused haemodynamic collapse and was converted electrically. During diagnostic investigation, echocardiography revealed evidence of right ventricular dysfunction. She underwent risk stratification and sustained monomorphic VT was easily induced during electrophysiology study. An implantable cardioverter-defibrillator (ICD) device was subsequently implanted, but she died suddenly three months later. ICD device interrogation did not reveal any arrhythmic event and death was attributed to carbon monoxide poisoning