Proliferating Trichilemmal Tumour (PTT) is a rapidly
growing large cutaneous adnexal neoplasm. Although
biologically considered as benign, it may be locally
aggressive. Malignant transformation of these lesions,
known as Malignant Proliferating Trichilemmal
Tumour (MPTT) has rarely been reported. So far in the
literature, only 39 well-documented cases of MPTT
have been reported. MPTT has been stated to be a
neoplasm of the older age group according to review of
the literature. We present a case of MPTT in a young
male. A 25 year old male presented with a scalp
swelling of 2 years duration with a recent rapid
enlargement. The swelling was excised and
histopathological examination of the excised
specimen revealed features of MPTT. The differential
diagnosis of MPTTis squamous cell carcinoma as both
share common features. Accurate diagnosis of MPTT
is essential since it has a tendency to metastasize and
recur more frequently than squamous cell carcinoma