Sturge-Weber syndrome (SWS) also known as
encephalotrigeminal angiomatosis. It is a
neurocutaneous syndrome, characterized by a
facial vascular birthmark and neurological
abnormalities. An ipsilateral or bilateral facial
cutaneous vascular malformation Port Wine Stain
(PWS) usually affects the upper face. Other
clinical manifestations are seizures, glaucoma,
hemiparesis, mental retardation and delayed
developmental milestones. The main objective of
this case report is to unravel such a rarest syndrome
with bilateral port-wine stain, which has
intraoral manifestation of pyogenic granuloma
involving gingiva in an 11 year old boy