The congenital radius pseudarthrosis is a rare condition which’s treatment is difficult. There were many reported surgical options for this situation. One of them is construction of one-bone in forearm. Here, we presented a seven years-old boy who has instability and defective congenital radius pseudarthrosis in forearm that treated with side-to-side distal radioulnar bifurcation synostosis technique preserving the distal radioulnar joint, and obtained good functional results