Scimitar Syndrome Issued from a Consanguineous Marriage: A Rare Congenital Cardiomyopathy

We present here a rare case of Scimitar syndrome on a full-term newborn female issued from consanguineous marriage and diagnosed at the age of two months who was suffering from polypnea since the age of two weeks. She was admitted at the age of two months for polypnea, non-dysmorphic facies, healthy systemic arterial tension, regular pulse, but the family history raises that before her birth, two newborns respectively boy and girl died both at an early age with dilated cardiomyopathy. After hospitalization, we realized chest radiography, which has shown opaque right lung and suspicion of scimitar syndrome. After that, an echocardiogram was performed, showing severe hypoplasia of the right pulmonary artery with pulmonary hypertension. The Thoracic computed tomography confirmed the diagnosis by revealing hypoplasia of the right pulmonary artery with pulmonary arterial hypertension, right pulmonary hypoplasia (bilobar), and abnormal partial right pulmonary venous return toward the vena cava under the diaphragm

RARE COR TRIATRIUM COMPLICATIONS : CASES REPORTS AND LITERATURE REVIEW

Cor triatriatum, est une anomalie cardiaque congénitale impliquant une membrane fibromusculaire qui divise même l'oreillette gauche ou la droite en 2 chambres.Cette anomalie n'a été rapportée que chez 0,1% à 0,4% des patients atteints de cardiopathie congénitale. La plupart des patients sont diagnostiqués avec la condition dans la petite enfance ou l'enfance; les cas adultes sont rares.Nous décrivons trois complications rares du cor triatriatum. Le premier cas concerne une embolie pulmonaire compliquant un cor triatrium dextrum chez un homme de 44 ans, ce qui n'a jamais été rapporté, du moins à notre connaissance. Il a subi une résection corrective de la membrane et a été asymptomatique par la suite.Le deuxième cas concerne la mort subite d'un nourrisson de 9 mois cor triatrium sinistrumLe dernier est un patient de 45 ans environ admis pour fibrillation auriculaire révélant un triatrium cornéen

Pancreatic surgery outcomes: multicentre prospective snapshot study in 67 countries

Background: Pancreatic surgery remains associated with high morbidity rates. Although postoperative mortality appears to have improved with specialization, the outcomes reported in the literature reflect the activity of highly specialized centres. The aim of this study was to evaluate the outcomes following pancreatic surgery worldwide.Methods: This was an international, prospective, multicentre, cross-sectional snapshot study of consecutive patients undergoing pancreatic operations worldwide in a 3-month interval in 2021. The primary outcome was postoperative mortality within 90 days of surgery. Multivariable logistic regression was used to explore relationships with Human Development Index (HDI) and other parameters.Results: A total of 4223 patients from 67 countries were analysed. A complication of any severity was detected in 68.7 percent of patients (2901 of 4223). Major complication rates (Clavien-Dindo grade at least IIIa) were 24, 18, and 27 percent, and mortality rates were 10, 5, and 5 per cent in low-to-middle-, high-, and very high-HDI countries respectively. The 90-day postoperative mortality rate was 5.4 per cent (229 of 4223) overall, but was significantly higher in the low-to-middle-HDI group (adjusted OR 2.88, 95 per cent c.i. 1.80 to 4.48). The overall failure-to-rescue rate was 21 percent; however, it was 41 per cent in low-to-middle-compared with 19 per cent in very high-HDI countries.Conclusion: Excess mortality in low-to-middle-HDI countries could be attributable to failure to rescue of patients from severe complications. The authors call for a collaborative response from international and regional associations of pancreatic surgeons to address management related to death from postoperative complications to tackle the global disparities in the outcomes of pancreatic surgery (NCT04652271; ISRCTN95140761)