2 research outputs found
Π‘ΠΈΠ½ΡΡΠ½ΡΠΉ Π³ΠΈΡΡΠΈΠΎΡΠΈΡΠΎΠ· (Π±ΠΎΠ»Π΅Π·Π½ΡΠ ΠΎΠ·Π°ΠΈ - ΠΠΎΡΡΠΌΠ°Π½Π°): ΠΊΠ»ΠΈΠ½ΠΈΡΠ΅ΡΠΊΠΎΠ΅ Π½Π°Π±Π»ΡΠ΄Π΅Π½ΠΈΠ΅
The authors characterized a heterogeneous group of a rare disease - Langerhans and non-Langerhans cell histiocytosis,
and analyzed key differential and diagnostic differences between these forms of the disease. A very rare case of non-
Langerhans cell histiocytosis (Rosai-Dorfman disease) in a female patient aged 63 with the subsequent spontaneous
regression of eruptions was described. Key skin manifestations of the Rosai-Dorfman disease included papular eruptions
of the typical intense pink color with a yellowish and brown tint. Morphologic changes were characterized by proliferation
of histiocytes and accumulation of different lipids and pentalamellar markers (S-100 protein, Π‘D 14, Π‘D 68, lysozyme)
in their cytoplasm. Though the Rosai-Dorfman disease usually involves lymph nodes, this case was characterized by
unaffected nodular structures.ΠΡ
Π°ΡΠ°ΠΊΡΠ΅ΡΠΈΠ·ΠΎΠ²Π°Π½Π° Π½Π΅ΠΎΠ΄Π½ΠΎΡΠΎΠ΄Π½Π°Ρ Π³ΡΡΠΏΠΏΠ° ΡΠ΅Π΄ΠΊΠΈΡ
Π³ΠΈΡΡΠΈΠΎΡΠΈΡΠΎΠ·ΠΎΠ² Π»Π°Π½Π³Π΅ΡΠ³Π°Π½ΡΠΎΠ²ΠΎΠ³ΠΎ ΠΈ Π½Π΅Π»Π°Π½Π³Π΅ΡΠ³Π°Π½ΡΠΎΠ²ΠΎΠ³ΠΎ ΡΠΈΠΏΠΎΠ²;
ΠΏΡΠΎΠ°Π½Π°Π»ΠΈΠ·ΠΈΡΠΎΠ²Π°Π½Ρ ΠΈΡ
ΠΎΡΠ½ΠΎΠ²Π½ΡΠ΅ Π΄ΠΈΡΡΠ΅ΡΠ΅Π½ΡΠΈΠ°Π»ΡΠ½ΠΎ-Π΄ΠΈΠ°Π³Π½ΠΎΡΡΠΈΡΠ΅ΡΠΊΠΈΠ΅ ΡΠ°Π·Π»ΠΈΡΠΈΡ. ΠΠΏΠΈΡΠ°Π½ΠΎ ΡΡΠ΅Π·Π²ΡΡΠ°ΠΉΠ½ΠΎ ΡΠ΅Π΄ΠΊΠΎΠ΅
Π½Π°Π±Π»ΡΠ΄Π΅Π½ΠΈΠ΅ Π³ΠΈΡΡΠΈΠΎΡΠΈΡΠΎΠ·Π° Π½Π΅Π»Π°Π½Π³Π΅ΡΠ³Π°Π½ΡΠΎΠ²ΠΎΠ³ΠΎ ΡΠΈΠΏΠ° (Π±ΠΎΠ»Π΅Π·Π½Ρ Π ΠΎΠ·Π°ΠΈ - ΠΠΎΡΡΠΌΠ°Π½Π°) Ρ ΠΏΠ°ΡΠΈΠ΅Π½ΡΠΊΠΈ 63 Π»Π΅Ρ Ρ
ΠΏΠΎΡΠ»Π΅Π΄ΡΡΡΠΈΠΌ ΡΠΏΠΎΠ½ΡΠ°Π½Π½ΡΠΌ ΡΠ΅Π³ΡΠ΅ΡΡΠΎΠΌ Π²ΡΡΡΠΏΠ°Π½ΠΈΠΉ. ΠΡΠ½ΠΎΠ²Π½ΡΠ΅ ΠΊΠΎΠΆΠ½ΡΠ΅ ΠΏΡΠΎΡΠ²Π»Π΅Π½ΠΈΡ Π±ΠΎΠ»Π΅Π·Π½ΠΈ Π ΠΎΠ·Π°ΠΈ - ΠΠΎΡΡΠΌΠ°Π½Π°
Π±ΡΠ»ΠΈ ΠΏΡΠ΅Π΄ΡΡΠ°Π²Π»Π΅Π½Ρ ΠΏΠ°ΠΏΡΠ»Π΅Π·Π½ΡΠΌΠΈ Π²ΡΡΡΠΏΠ°Π½ΠΈΡΠΌΠΈ ΡΠΈΠΏΠΈΡΠ½ΠΎΠ³ΠΎ Π½Π°ΡΡΡΠ΅Π½Π½ΠΎΠ³ΠΎ ΡΠΎΠ·ΠΎΠ²ΠΎΠ³ΠΎ ΡΠ²Π΅ΡΠ° Ρ ΠΆΠ΅Π»ΡΠΎΠ²Π°ΡΠΎ-ΠΊΠΎΡΠΈΡΠ½Π΅Π²ΡΠΌ
ΠΎΡΡΠ΅Π½ΠΊΠΎΠΌ. ΠΠΎΡΡΠΎΠ»ΠΎΠ³ΠΈΡΠ΅ΡΠΊΠΈΠ΅ ΠΈΠ·ΠΌΠ΅Π½Π΅Π½ΠΈΡ Ρ
Π°ΡΠ°ΠΊΡΠ΅ΡΠΈΠ·ΠΎΠ²Π°Π»ΠΈΡΡ ΠΏΡΠΎΠ»ΠΈΡΠ΅ΡΠ°ΡΠΈΠ΅ΠΉ Π³ΠΈΡΡΠΈΠΎΡΠΈΡΠΎΠ² ΠΈ Π½Π°ΠΊΠΎΠΏΠ»Π΅Π½ΠΈΠ΅ΠΌ
Π² ΠΈΡ
ΡΠΈΡΠΎΠΏΠ»Π°Π·ΠΌΠ΅ ΡΠ°Π·Π»ΠΈΡΠ½ΡΡ
Π»ΠΈΠΏΠΈΠ΄ΠΎΠ², ΠΏΠ΅Π½ΡΠ°Π»Π°ΠΌΠ΅Π»Π»ΡΡΠ½ΡΡ
ΠΌΠ°ΡΠΊΠ΅ΡΠΎΠ² (ΠΏΡΠΎΡΠ΅ΠΈΠ½ S-100, Π‘D14, Π‘D 68, Π»ΠΈΠ·ΠΎΡΠΈΠΌ).
ΠΠ΅ΡΠΌΠΎΡΡΡ Π½Π° ΡΠΎ ΡΡΠΎ Π±ΠΎΠ»Π΅Π·Π½Ρ Π ΠΎΠ·Π°ΠΈ - ΠΠΎΡΡΠΌΠ°Π½Π°, ΠΊΠ°ΠΊ ΠΏΡΠ°Π²ΠΈΠ»ΠΎ, ΠΏΡΠΎΡΠ΅ΠΊΠ°Π΅Ρ Ρ ΠΏΠΎΡΠ°ΠΆΠ΅Π½ΠΈΠ΅ΠΌ Π»ΠΈΠΌΡΠΎΡΠ·Π»ΠΎΠ²,
ΠΎΡΠ»ΠΈΡΠΈΡΠ΅Π»ΡΠ½ΠΎΠΉ ΠΎΡΠΎΠ±Π΅Π½Π½ΠΎΡΡΡΡ Π΄Π°Π½Π½ΠΎΠ³ΠΎ Π½Π°Π±Π»ΡΠ΄Π΅Π½ΠΈΡ ΡΠ²ΠΈΠ»ΠΎΡΡ ΠΎΡΡΡΡΡΡΠ²ΠΈΠ΅ Π²ΠΎΠ²Π»Π΅ΡΠ΅Π½ΠΈΡ Π½ΠΎΠ΄ΡΠ»ΡΡΠ½ΡΡ
ΡΡΡΡΠΊΡΡΡ