14,034 research outputs found
The meteorologically driven circulation in mid-Chesapeake Bay
Utilizing 20 days of sea level elevation and current records in mid-Chesapeake Bay, the frequency structure of the meteorological forcing is investigated. For periods longer than 8 days the residual sea level inside the Bay is coupled to the coastal elevation forced by the onshore-offshore component of the wind, while at the 3–8 day scale the system was driven by the local longitudinal wind component. It is suggested, however, that the partition of energy between the longitudinal and lateral wind components may determine whether the Bay responds locally to the wind or to the coastal elevations. The 2–2.5 day sea level oscillations could not be identified with a seiche in the Bay; their source is not clear, but the atmospheric pressure is a possibility.The vertical structure of the residual currents through two cross-sections shows that the layers in the upper 8 m are directly driven by the wind, while in the deeper layers the flow is opposite the wind as a result of the surface slope associated with it. The lag in this counter flow increases from the bottom up and is explained in terms of the phase lag of the surface slope response to the wind and the depth dependence of the current response to the wind
GM1 Gangliosidosis, Late Infantile Onset Dystonia, and T2 Hypointensity in the Globus Pallidus and Substantia Nigra
BACKGROUND: GM1 gangliosidosis is a rare disease due to mutations in the GLB1 gene and
autosomal recessive deficiency of b-galactosidase. There is considerable overlap between classical phenotypes and clinical and imaging findings, which are often difficult to interpret. PATIENT: The patient in this study had dysmorphism, dysostosis, progressive dystonia, and T2 hypointensity in the basal ganglia. Partially similar clinical and radiologic findings were described previously in two reports. CONCLUSIONS: T2 hypointensity in the
globus pallidus should, in the appropriate clinical setting, lead to consideration of thediagnosis of GM1 gangliosidosis
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