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Myeloid Sarcoma in the Central Nervous System: Case Report and Review of the Literature
Mijeloidni sarkomi su rijetke pojavnosti uglavnom mijeloblastiÄne leukemije. Njihova pojava u srediÅ”njem živÄanom sustavu je iznimna, pa je dotiÄna literatura danas ograniÄena na studije pojedinih sluÄajeva. Mi opisujemo jo. jedan sluÄaj, dok je pregled literature poslužio kako bismo ispitali znaÄajke i moguÄnosti lijeÄenja mijeloidnog sarkoma srediÅ”njega živÄanog sustva. U žene stare 61 godinu s akutnom mijeloblastiÄnom leukemijom (FAB M5) i progresivnom lijevostranom hemiparezom utvrÄena je desnostrano parieto-okcipitalno epiduralno oÅ”teÄenje koje je sliÄilo meningiomu. UÄinjena je djelomiÄna resekcija koja je otkrila mijeloidni sarkom. Pregledom literature utvrdili smo 44 sluÄaja s dostatnim opisom dijagnoze, lijeÄenja i praÄenja do jedne godine. Kod tih bolesnika primijenjeni su razliÄiti naÄini lijeÄenja. MeÄutim, bolesnici su imali najbolji postotak jednogodiÅ”njeg preživljenja kad je protokol lijeÄenja ukljuÄivao sustavnu kemoterapiju ili zraÄenje.Myeloid sarcomas are rare manifestations of mainly myeloblastic leukemia. Their occurrence in the central nervous system is exceptional and current literature is limited to case studies. A case is added herewith and a review was performed to investigate clinical characteristics and treatment options of central nervous system myeloid sarcoma. A 61-year-old female with acute myeloblastic leukemia (FAB M5) and progressive left sided hemiparesis showed a right parieto-occipital epidural lesion mimicking meningioma. Partial resection was performed to reveal a myeloid sarcoma. Reviewing the literature we identified 44 cases with sufficient description of the diagnosis, treatment and follow up to one year. In these patients different treatment regimens were applied. However, when systemic chemotherapy or irradiation was included in the treatment regimen, patients showed the best 1-year survival proportion