The clinical value of the auditory steady state response for early diagnosis and amplification for infants (0-8 months) with hearing loss

There has always been a need for objective tests that assess auditory function in infants, young children, and/or any patient whose development level precludes the use of behavioral audiometric techniques. Although the Auditory Brainstem Response (ABR) is seen as the ‘gold standard’ in the field of objective audiometry, it presents with its own set of limitations. The Auditory Steady State Response (ASSR) has gained considerable attention and is seen as a promising addition to the AEP ‘family’ to address some of the limitations of the ABR. The ASSR promises to estimate all categories of hearing loss (mild to profound) in a frequency specific manner. It also indicates to the possibility to validate hearing aid fittings by determining functional gain of hearing aids by determining unaided and aided ASSR thresholds. An exploratory research design was selected in order to compare unaided thresholds, obtained through the use of three different procedures – ABR, ASSR and behavioral thresholds. Aided thresholds were also obtained and compared with two procedures – the aided ASSR (measured and predicted) and aided behavioral threshold. The results indicated that both the ABR (tone burst and click) and ASSR provided a reasonable estimation of the subsequently obtained behavioral audiograms. The ASSR, however, approximated the behavioral thresholds closer than the ABR and were furthermore able to quantify hearing thresholds accurately for subjects with severe and profound hearing losses. The result indicated further that the ASSR can be instrumental in the validation process of hearing aid fittings in infants. These results demonstrated however, that the ASSR measured thresholds underestimate the aided behavioral thresholds and the aided ASSR predicted thresholds overestimate the aided behavioral thresholds. The research concluded that the ASSR is useful in estimating frequency-specific behavioral thresholds accurately in infants and validating hearing aid fittings. Until evidence is sufficient to recommend the ASSR as primary electrophysiological measure of hearing in infants, the ASSR should be used in conjunction with the ABR – following a test battery approach in the diagnostic process of hearing loss in infants. The ASSR further shows great promise in validating hearing aid fittings, but this specific application of the ASSR needs further research evidence on large groups to validate the procedure.Dissertation (Master of Communication Pathology)--University of Pretoria, 2007.Speech-Language Pathology and Audiologyunrestricte

Does parental experience of the diagnosis and intervention process differ for children with auditory neuropathy?

OBJECTIVES : This study compared parental experience of the audiological diagnosis and intervention process in children with auditory neuropathy spectrum disorder and sensory neural hearing loss. METHODS : A matched group survey was used with parents of children with auditory neuropathy spectrum disorder (ANSD) matched with a control group of parents and children with sensorineural hearing loss (SNHL). The two groups were matched in terms of the child’s gender, age, amplifications used, social background and utilisation of private or public health care sectors. An interview questionnaire, consisting of 45 questions in six categories (1. biographic information, 2. experiences of audiological diagnosis, 3. hearing aid benefit, 4. parental experience of the rehabilitation decision making process, 5. parental needs for emotional support and 6. parental needs for information) using a 5-point Likert scale for categories 2–7, was administered by the same audiologist. RESULTS : Children with ANSD experienced a significantly longer waiting period from diagnosis to hearing aid fitting (p = 0.025) and/or cochlear implantation (p = 0.036). Parents of children with ANSD reported significantly different experiences of the diagnostic process (p = 0.001) with poorer understanding of the diagnosis and reporting insufficient time allowed for asking questions. During the rehabilitation decision-making process 47% of parents with ANSD children (vs. 0% of parents with SNHL children) reported receiving conflicting information. Parents of children with ANSD were also less likely to recommend hearing aids to other parents. Information needs were similar between groups. CONCLUSIONS : Parents of children with ANSD have different experiences and greater uncertainty during the diagnostic and rehabilitation process. Providing regular consultation and structured timelines through the diagnostic process and decision-making process may facilitate this process with less uncertainty.http://www.elsevier.com/locate/ijporlhb201