30 research outputs found

    Vigilance and vigilantes: thinking psychoanalytically about anti-paedophile action

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    This paper applies a psychoanalytic approach to the protests of members of `Residents Against Paedophiles' on the Paulsgrove estate in Portsmouth, UK, in August 2000. It sets these in the context of the strains existing in the British government's policy on sexual offenders. It is argued that the protests demonstrate the existence of links between a vigilante state of mind and the `mind of state' that makes community members responsible for crime management. Evidence is provided by the protesters' fabrication of a `mental list' of convicted sex offenders that mimicked the official register. The paper concludes that access to information does not always have the effect of containing adults in such a way that enhances their capacity to act as `responsible' citizens

    Expanding the phenotype of GMPPB mutations

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    Dystroglycanopathies are a heterogeneous group of diseases with a broad phenotypic spectrum ranging from severe disorders with congenital muscle weakness, eye and brain structural abnormalities and intellectual delay to adult-onset limb-girdle muscular dystrophies without mental retardation. Most frequently the disease onset is congenital or during childhood. The exception is FKRP mutations, in which adult onset is a common presentation. Here we report eight patients from five non-consanguineous families where next generation sequencing identified mutations in the GMPPB gene. Six patients presented as an adult or adolescent-onset limb-girdle muscular dystrophy, one presented with isolated episodes of rhabdomyolysis, and one as a congenital muscular dystrophy. This report expands the phenotypic spectrum of GMPPB mutations to include limb-girdle muscular dystrophies with adult onset with or without intellectual disability, or isolated rhabdomyolysis
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