Is arrhythmogenic right ventricular cardiomyopathy a paediatric problem too?

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a heart muscle disease that is often familial, characterized by arrhythmias of right ventricular origin, due to transmural fatty or fibrofatty replacement of atrophic myocardium. ARVC is usually diagnosed in the clinical setting between 20 and 40 years of age. The disease is seldom recognised in infancy or under the age of 10, probably because the clinical expression of the disease is normally postponed to youth and adulthood. This review focuses its attention to the pediatric age, defined as the period of life raging from birth to 18 years. During this span of life, ARVC is not so rare as previously supposed and can be identified by applying the same diagnostic criteria proposed for the adult. Ventricular arrhythmias range from isolated ventricular arrhythmias to sustained ventricular tachycardia and fibrillation. Children and adolescents with ARVC must be carefully evaluated and followed-up especially when a family positive history is present, taking into account the high probability during this life-period that asymptomatic affected patients become symptomatic or that arrhythmias worsen during follow-up. The recent identification of the first defective gene opens new avenues for the early identification of affected subjects even when asymptomatic.peer-reviewe

Finite-size analysis of the Fermi liquid properties of the homogeneous electron gas

We analyze the extrapolation to the thermodynamic limit of Fermi liquid properties of the homogeneous electron gas in two and three dimensions. Using field theory, we explicitly calculate finite-size effects of the total energy, the renormalization factor, and the effective mass at the Fermi surface within the random phase approximation (RPA) and discuss the validity for general metallic systems.Comment: 6 page

Comparing TOPEX TEC measurements with IRI predictions

TEC values obtained from TOPEX satellite were compared with the International Reference Ionosphere (IRI) 2001 model estimates. The present work also shows results of the IRI model with the option of a new topside electron density distribution (NeQuick model). TOPEX TEC measurements, which include years of high and middle to low solar activity (2000 and 2004), were analyzed by binning the region covered by the satellite (±66°) every five degrees of modip. In general, there is good agreement between IRI predictions and Topex measurements. Cases with large disagreements are observed at low and high latitudes during high solar activity. Comparing the model predictions using the default IRI2001 model and the NeQuick topside option show that the default IRI 2001 version represents the observed data in a more realistic way, but appears to be less reliable at high and low latitudes in some cases.Fil: Migoya Orue, Yenca Olivia. Universidad Tecnológica Nacional; ArgentinaFil: S.M. Radicella. Aeronomy and Radiopropagation Laboratory; ItaliaFil: P. Coïsson. Aeronomy and Radiopropagation Laboratory; ItaliaFil: Ezquer, Rodolfo Gerardo. Universidad Nacional de Tucumán. Facultad de Ciencias Exactas y Tecnología. Departamento de Física. Laboratorio de Ionósfera; Argentina. Consejo Nacional de Investigaciones Científicas y Técnicas. Centro Científico Tecnológico Conicet - Tucumán; ArgentinaFil: Nava, B.. Aeronomy and Radiopropagation Laboratory; Itali

The faster the narrower: characteristic bulk velocities and jet opening angles of Gamma Ray Bursts

The jet opening angle theta_jet and the bulk Lorentz factor Gamma_0 are crucial parameters for the computation of the energetics of Gamma Ray Bursts (GRBs). From the ~30 GRBs with measured theta_jet or Gamma_0 it is known that: (i) the real energetic E_gamma, obtained by correcting the isotropic equivalent energy E_iso for the collimation factor ~theta_jet^2, is clustered around 10^50-10^51 erg and it is correlated with the peak energy E_p of the prompt emission and (ii) the comoving frame E'_p and E'_gamma are clustered around typical values. Current estimates of Gamma_0 and theta_jet are based on incomplete data samples and their observed distributions could be subject to biases. Through a population synthesis code we investigate whether different assumed intrinsic distributions of Gamma_0 and theta_jet can reproduce a set of observational constraints. Assuming that all bursts have the same E'_p and E'_gamma in the comoving frame, we find that Gamma_0 and theta_jet cannot be distributed as single power-laws. The best agreement between our simulation and the available data is obtained assuming (a) log-normal distributions for theta_jet and Gamma_0 and (b) an intrinsic relation between the peak values of their distributions, i.e theta_jet^2.5*Gamma_0=const. On average, larger values of Gamma_0 (i.e. the "faster" bursts) correspond to smaller values of theta_jet (i.e. the "narrower"). We predict that ~6% of the bursts that point to us should not show any jet break in their afterglow light curve since they have sin(theta_jet)<1/Gamma_0. Finally, we estimate that the local rate of GRBs is ~0.3% of all local SNIb/c and ~4.3% of local hypernovae, i.e. SNIb/c with broad-lines.Comment: 15 pages, 8 figures, 1 table. Accepted for publication in MNRA

T-violation in Kμ3K_{\mu3} decay in a general two-Higgs doublet model

We calculate the transverse muon polarization in the $K^+_{\mu3}$ process arising from the Yukawa couplings of charged Higgs boson in a general two-Higgs doublet model where spontaneous violation of CP is presentComment: 6 pages, latex, accepted for publication in Phys. Rev.

Rate constant for the reaction NH2 + NO from 216 to 480 K

The absolute rate constant was measured by the technique of flash photolysis-laser induced fluorescence (FP-LIF). NH2 radicals were produced by the flash photolysis of ammonia and the fluorescent NH2 photons were measured by multiscaling techniques. At each temperature, the results were independent of variations in total pressure, and flash intensity. The results are compared with previous determinations using the techniques of mass spectrometry, absorption spectroscopy, laser absorption spectroscopy, and laser induced fluorescence. The implications of the results are discussed with regard to combustion, post combustion, and atmospheric chemistry. The results are also discussed theoretically