3 research outputs found
Congenital Nasopharyngeal Teratoma in a Neonate
Background: Congenital germ cell tumors are uncommon. The most common
site of teratoma is in the sacrococcygeal region. Teratoma arising from
the head and neck comprises less than 10% of reported cases and of
these, nasopharyngeal lesions are rare. Teratomas are generally benign,
and have a well recognized clinical and histopathological entity. We
present a case of nasopharyngeal teratoma (NPT) associated with a wide
cleft palate. Case Presentation: A 20 day old female neonate with a
teratoma of the nasopharyngeal area, and wide cleft palate was referred
to our center. The protruded mass which measured 6x4x3cm, was of soft
consistency, blocked the airway, and prevented oral feeding.
Preoperative evaluation and imaging was performed and mass was excised
2 days after admission. Pathology revealed a well-differentiated mature
solid teratoma (hairy polyp). The patient had no complication in the
post-operative period. Cleft palate was surgically repaired when 2
years old. She is now a six year old girl with normal development.
Conclusion: Congenital nasopharyngeal teratomas are usually benign.
Surgery is the treatment of choice, and should be undertaken on an
urgent basis, especially in a patient who presents with signs and
symptoms of airway obstruction
Diphallus: Report on Six Cases and Review of the Literature
Background: Diphallus is an extremely rare anomaly. Numerous
associated genitourinary, gastrointestinal and other anomalies have
been described with diphallus. These patients need several
investigations, and finally surgical intervention. Cases Presentation:
In this report we discuss six patients with diphallus which evaluated
retrospectively. Five patients had complete diphallia, and one had
bifid diphallus. Meatus was normal in 3, hypospadiac in 2, and
epispadiac in one patient. The most common associated anomaly was bifid
scrotum (5 cases), and other common anomalies consisted of bladder
duplication (3 cases), imperforate anus (2 cases), and hypospadias (2
cases). Phalloplasty was performed for all but one. Conclusion: All
the patients with urethral duplication have to be evaluated carefully
because of the high incidence of other systemic anomalies
Abdominal Inflammatory Myofibroblastic Tumor: Report on Four Cases and Review of Literature
Background:The Abdominal Inflammatory Myofibroblastic Tumor (AIMT) is a
rare tumor with unknown etiology which usually occurs in children and
adolescents. It is composed of myofibroblastic spindle cells intermixed
with inflammatory cells. We present four cases of AIMT. Cases
Presentation: We herein present four cases of AIMT in different ages
(range: 3.5 to 13 years) and in different organs (stomach,
periduodenal, mesenteric, and colon). There were two females and two
males. The main symptoms were abdominal pain/mass/obstruction,
vomiting, and weight loss. In all four patients, diagnosis was made by
laparatomy and pathologic examination of excised mass lesion. Three
patients underwent complete excision and no residual disease was
present, one patient received chemotherapy due to tumor recurrences.
The patients were followed up in average for four years. Conclusion: As
the imaging and laboratory tests are non-specific, the diagnosis of
AIMT is rarely made before surgery. AIMT should, therefore, be
considered when a mass arises in an unusual location in the pediatric
age group. Complete surgical resection should be performed whenever
possible and the child should be kept on long-term follow-up