Dorsosacral myxoma mimicking Pilonidal Sinus

Introduction: Sacrococcygeal Pilonidal Sinus Disease has a classical appearance. Rarely unrelated pathology may occur in the natal cleft. Methods: Case report with follow up. Results: 40 year old male with a 2 centimeter dorsosacral mass underwent excision with modified Limberg flap. Pre-operative Magnetic Resonance Imaging reported a pilonidal sinus without fistula opening. Histological examination revealed the mass to be a myxoma. Conclusion: We present a quite uncommon case of postsacral myxoma, mimicking a pilonidal sinus. If midline pits are missing in uninflamed disease, there may be some diagnostic challenge to distinguish a – rare – myxoma from common Pilonidal Sinus Disease