Supravalvar aortic stenosis as well as peripheral pulmonary stenosis are rare forms of congenital
heart disease, which occur, however, relatively frequently in association. This article reports and
discusses the classical findings of SVAS and PPS upon clinical examination and imaging in a sixyear-old
girl that presented with repeated respiratory tract infections and failure to thrive.peer-reviewe

Gupta, S.K.

Kahr, P.C.

Kothari, Shyam S.

Ramakrishnan, S.

OAR@UM

PubMed Central

English

Balloon dilation angioplasty of peripheral pulmonary stenosis associated with Williams syndrome.

Forty-one years of surgical experience with congenital supravalvular aortic stenosis. J Thorac Cardiovasc Surg.

Issues and outcomes in the management of supravalvar aortic stenosis. The Annals of Thoracic Surgery.

Natural history of supravalvular aortic stenosis and pulmonary artery stenosis.

Outcomes after primary transcatheter therapy in infants and young children with severe bilateral peripheral pulmonary artery stenosis. Circulation: Cardiovascular Interventions.

The natural course of supravalvar aortic stenosis and peripheral pulmonary artery stenosis in Williams's syndrome. Br Heart J.

Classical supravalvar aortic stenosis and peripheral pulmonary stenosis