10 research outputs found
Motor neuron intrinsic and extrinsic mechanisms contribute to the pathogenesis of FUS-associated amyotrophic lateral sclerosis
- Author
- A Belly
- A Calvo
- A Conte
- A Guilbot
- A Hubers
- A King
- A Sharma
- Albert C. Ludolph
- AM Blokhuis
- B Hu
- B Oosthuyse
- B Swinnen
- BJ Turner
- C Vance
- C Verbeeck
- CF Boerkoel
- CF Sephton
- CG Carlson
- Christian Haass
- Clotilde Lagier-Tourenne
- CS Gillespie
- CS Lobsiger
- D Baumer
- D Bergemalm
- D Dormann
- D Dormann
- D Dormann
- Dorothee Dormann
- E Kabashi
- Erik Storkebaum
- F Tian
- FA Court
- Frédérique René
- G Shiihashi
- GA Nicholson
- H Deng
- H Qiu
- H Tsuiji
- H Wils
- HA Bowden
- Hajer El Oussini
- HS Kwon
- I Wegorzewska
- IR Mackenzie
- IR Mackenzie
- J Guo
- J Japtok
- J Rossi
- J Scekic-Zahirovic
- J Zenker
- JC Mitchell
- Jelena Scekic-Zahirovic
- Jérôme Sinniger
- K Adlkofer
- K Angeby-Moller
- K Yamanaka
- Kevin Drenner
- Kira Allmeroth
- KS Graffmo
- L Dupuis
- L Dupuis
- Luc Dupuis
- M Cerghet
- M Horn
- M Marino
- M Morlando
- M Neumann
- M Neumann
- M Schoen
- M Sedelis
- M Suarez-Calvet
- MA Esmaeili
- Marina Wagner
- MC Kiernan
- ME Gurney
- ML Tradewell
- N Ichiyanagi
- N Suzuki
- OM Peters
- R Fujii
- R Hussain
- RP Skoff
- S Boillee
- S Boillee
- S Dini Modigliani
- S Saxena
- S Sun
- S Waibel
- S Waibel
- SC Ling
- SH Kang
- SH Kang
- Sina Mersmann
- SM Lim
- Stéphane Dieterlé
- Sylvie Dirrig-Grosch
- T Hatzipetros
- T Philips
- T Saito
- TD Heiman-Patterson
- TJ Kwiatkowski Jr
- V Swarup
- W Masocha
- WW Motley
- XH Wang
- Y Ito
- Y Kino
- Y Lee
- Y Zhou
- YF Xu
- Ying Sun
- ZY Zou
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
CuII(atsm) improves the neurological phenotype and survival of SOD1G93A mice and selectively increases enzymatically active SOD1 in the spinal cord
- Author
- AE Renton
- AF Hottinger
- BA Gingras
- BR Roberts
- BR Roberts
- CP Soon
- DA Bosco
- DR Rosen
- E Tokuda
- E Tokuda
- E Tokuda
- EJ McAllum
- F Li
- HJ Forman
- IA Trounce
- JA Rumfeldt
- JB Hilton
- JB Hilton
- JP Holland
- JR Williams
- K Wada
- KS Graffmo
- LJ Hayward
- LW Hung
- M Chattopadhyay
- M Ikawa
- M Ikawa
- M Ikawa
- M Son
- ME Gurney
- ME Gurney
- OA Andreassen
- P Ip
- P Vehvilainen
- PC Wong
- PS Donnelly
- S Marklund
- S Nagano
- SM Lynch
- TW Rhoads
- VK Mulligan
- W Tan
- Y Furukawa
- Y Yoshii
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Conformational specificity of the C4F6 SOD1 antibody; low frequency of reactivity in sporadic ALS cases
- Author
- A Durazo
- AG Estévez
- AK Museth
- CM Karch
- CM Karch
- CM Karch
- D Jaarsma
- D Jaarsma
- DA Bosco
- DA Bosco
- EL Shipp
- F Gros-Louis
- H-X Deng
- H-X Deng
- HX Deng
- J Ayers
- J Wang
- J Wang
- J-N Audet
- JB Cavanagh
- JN Keller
- KS Graffmo
- L Banci
- L Wang
- M Prudencio
- M Prudencio
- M Prudencio
- M Prudencio
- M Urushitani
- ME Gurney
- PA Jonsson
- PC Wong
- PJ Hart
- R Rakhit
- R Rakhit
- S Saxena
- SD Khare
- SV Seetharaman
- T Schmidlin
- TE Brotherton
- W Song
- Y Shi
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
TDP-43 or FUS-induced misfolded human wild-type SOD1 can propagate intercellularly in a prion-like fashion
- Author
- A Kerman
- AC Elden
- AE Renton
- C Gomes
- C Munch
- C Vance
- CK Bruns
- DA Bosco
- E Pokrishevsky
- EL Scotter
- EL Tudor
- F Gros-Louis
- GP Ritson
- GY Hsiung
- H Ilieva
- H Maruyama
- HN Liu
- HN Liu
- HX Deng
- IR Mackenzie
- J Choi
- J Deng
- JA Cassel
- JI Ayers
- JL Guo
- JM Ravits
- K Forsberg
- KD Foust
- KS Graffmo
- L Banci
- LI Grad
- LI Grad
- LI Grad
- M Jucker
- M Neumann
- M Udan-Johns
- M Urushitani
- M Urushitani
- ME Murray
- MT Lin
- OA Brady
- SB Prusiner
- T Arai
- T Hatzipetros
- T Nonaka
- T Sekiguchi
- TE Brotherton
- TJ Kwiatkowski Jr.
- W Wang
- WC Guest
- Y Furukawa
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Experimental transmissibility of mutant SOD1 motor neuron disease
- Author
- A Aguzzi
- A Taraboulos
- A-L Mougenot
- Adam DeBosier
- AG Dickinson
- Ben McMahon
- BR Brooks
- C Münch
- CM Karch
- D Jaarsma
- D Peretz
- DA Qualls
- David R. Borchelt
- DR Borchelt
- DR Borchelt
- F Clavaguera
- Guilian Xu
- J Ayers
- J Ayers
- J Ravits
- J Wang
- J Wang
- J Wang
- JA Johnston
- Jacob I. Ayers
- JC Bartz
- JM Ravits
- JR Fraser
- K Schneider
- KK Hsiao
- KS Graffmo
- L Banci
- L Monari
- LI Bruijn
- LI Grad
- M Bruce
- M Chattopadhyay
- M Meyer-Luehmann
- M Prudencio
- M Prudencio
- M Prudencio
- ME Gurney
- Morgan Koch
- MP McKinley
- PA Jonsson
- PA McBride
- PC Wong
- R Chia
- RA Bessen
- Susan Fromholt
- T Kanouchi
- ZA Oztug Durer
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Distinct conformers of transmissible misfolded SOD1 distinguish human SOD1-FALS from other forms of familial and sporadic ALS
- Author
- A Aguzzi
- A Kerman
- Adriana Sari
- AG Dickinson
- Ahmad Galaleldeen
- BI Giasson
- C Münch
- CK Glass
- D Jaarsma
- D Peretz
- DA Bosco
- David R. Borchelt
- E Pokrishevsky
- EE Bidhendi
- G Xu
- GG Kovács
- H Fraser
- H-X Deng
- J Ayers
- J Ayers
- J Ayers
- J Lewis
- J Wang
- J Wang
- Jacob I. Ayers
- Jeffrey Diamond
- Jonathan D. Glass
- K Forsberg
- KS Graffmo
- L Banci
- LG Goldfarb
- LI Grad
- LJ Reed
- Lyle W. Ostrow
- M Bruce
- M Chattopadhyay
- M Prudencio
- M Prudencio
- P Zetterström
- P. John Hart
- R Chia
- R Rakhit
- R Rakhit
- RA Bessen
- SA Ezzi
- Susan Fromholt
- SV Seetharaman
- TE Brotherton
- X Cao
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Extracellular wildtype and mutant SOD1 induces ER–Golgi pathology characteristic of amyotrophic lateral sclerosis in neuronal cells
- Author
- A Bertolotti
- A Preston
- A Tiwari
- Adam K. Walker
- AK Walker
- BJ Turner
- C Gomes
- C Münch
- D Ron
- DA Bosco
- Damian Spencer
- E Manders
- F Clavaguera
- F Gros-Louis
- GJ Doherty
- H Kikuchi
- H Nishitoh
- HP Phatnani
- J Lucocq
- JD Atkin
- JD Atkin
- Julie D. Atkin
- Justin Yerbury
- K Forsberg
- K Frutiger
- K Hirschberg
- K Roberts
- Kai Ying Soo
- KS Graffmo
- L Banci
- LI Grad
- M Nagai
- M Olczak
- M Schröder
- M Urushitani
- Manal A. Farg
- ME Gurney
- MJ Lindberg
- N Gonatas
- N Thayanidhi
- P Desplats
- P Sun
- P Zetterström
- Rafaa Zeineddine
- S Grimmer
- S Guareschi
- S Saxena
- S Takeuchi
- SA Ezzi
- TE Brotherton
- Vinod Sundaramoorthy
- Vy Hoang
- Y Furukawa
- Y Furukawa
- Z Darzynkiewicz
- Z Mourelatos
- ZAO Durer
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Misfolded SOD1 pathology in sporadic Amyotrophic Lateral Sclerosis
- Author
- A Kerman
- A-S Johansson
- AM Blokhuis
- B Paré
- BR Brooks
- C-F Tan
- CS Leblond
- D Bergemalm
- D Eisenberg
- D Pisa
- Da Bosco
- DW Mulder
- E Inoue
- E Pokrishevsky
- E Tokuda
- EF Pettersen
- F Gros-Louis
- F Gros-Louis
- F Gros-Louis
- GD Marco
- H Daoud
- H Stewart
- H-X Deng
- HN Liu
- J Brettschneider
- J Cooper-Knock
- JB Cavanagh
- JI Ayers
- JI Ayers
- JN Keller
- K Forsberg
- K Forsberg
- K Selmaj
- KS Graffmo
- LI Grad
- M Neumann
- M Synofzik
- M Urushitani
- Mehdi Ghasemi
- MP Hart
- P Zetterstrom
- P Zetterström
- PA Jonsson
- PA Jonsson
- PM Andersen
- PM Andersen
- R E. Mrak
- R Rakhit
- R Rakhit
- RW Strange
- RW Strange
- S Byrne
- S Chen
- S Guareschi
- SA Ezzi
- Sandrine Da Cruz
- TE Brotherton
- TT Rohn
- VV Belzil
- W Robberecht
- W Song
- WV Paesschen
- Y Ohta
- Y Okamoto
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Metal-deficient SOD1 in amyotrophic lateral sclerosis
- Author
- A Beleza-Meireles
- A Das
- A Tiwari
- A Tiwari
- A Tiwari
- AF Hottinger
- AG Reaume
- Anthony R. White
- BR Roberts
- C Cheroni
- CF Shaw 3rd
- CM Karch
- CP Soon
- D Jaarsma
- D Milardi
- DR Borchelt
- DR Rosen
- DW Cleveland
- E Naganska
- E Tokuda
- E Tokuda
- E Tokuda
- F Ding
- F Kitamura
- GJ Groeneveld
- H Takeuchi
- HA Dierick
- IP Ermilova
- JA Rodriguez
- James B. Hilton
- JJ Perry
- JP Crow
- JP Crow
- JS Beckman
- JS Valentine
- K Forsberg
- KA Trumbull
- KB Pierson
- KS Graffmo
- L Banci
- L Banci
- L Noto Di
- L Wang
- LI Bruijn
- LI Bruijn
- LJ Hayward
- M Basso
- M Chattopadhyay
- M Son
- M Watanabe
- MA Sahawneh
- MC Kiernan
- MF Beal
- ML Kennerson
- N Shibata
- P Ip
- P Zetterstrom
- PC Wong
- Peter J. Crouch
- PS Donnelly
- R Lalonde
- RW Strange
- S Petri
- SG Kaler
- SJ Weisberg
- TE Brotherton
- TJ Lyons
- TM Dawson
- TW Rhoads
- TW Rhoads
- V Swarup
- VD Longo
- VL Hodgkinson
- WI Vonk
- Y Furukawa
- YS Ho
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study
Does wild-type Cu/Zn-superoxide dismutase have pathogenic roles in amyotrophic lateral sclerosis?
- Author
- A Kerman
- A Tiwari
- AA Brasil
- AC Bowling
- B Pare
- B Zhao
- BA Keller
- BJ Turner
- C Soto
- CA Pardo
- CK Tsang
- CP Soon
- D Cruz-Garcia
- DA Bosco
- DB Medinas
- DM Taylor
- E Ekhtiari Bidhendi
- E Pokrishevsky
- E Yoshida
- F Gros-Louis
- FR Coelho
- GD Ghadge
- H Zhang
- HJ Forman
- HN Liu
- HN Liu
- HX Deng
- IN Zelko
- J Jacobsson
- J Sabado
- J Wang
- JB Hilton
- JH Park
- JI Ayers
- JJ Iliff
- JM McCord
- JN Audet
- JR Williams
- K Asayama
- K Forsberg
- K Forsberg
- K Fukada
- K Vijayalakshmi
- KM Killoy
- KS Graffmo
- L Wang
- L Winer
- LA Sturtz
- LI Bruijn
- LI Grad
- LJ Hayward
- M Polymenidou
- M Prudencio
- M Prudencio
- M Son
- M Son
- M Son
- M Uhlen
- M Urushitani
- M van Blitterswijk
- M Watanabe
- ME Gurney
- MJ Crisp
- MK Jaiswal
- MS Rotunno
- N Shibata
- N Shibata
- P Mondola
- P Mondola
- P Zetterstrom
- PA Jonsson
- PA Jonsson
- PA Jonsson
- PA Jonsson
- PA Jonsson
- PB Stathopulos
- PC Wong
- PM Andersen
- PM Andersen
- QX Dong
- R Rakhit
- RA Saccon
- RO Carare
- S Da Cruz
- S Da Mesquita
- S Guareschi
- S Takeuchi
- S Watanabe-Matsumoto
- SC Barber
- T Fujisawa
- TE Brotherton
- TJ Broering
- VC Culotta
- VK Mulligan
- W Peng
- W Robberecht
- WC Xu
- Y Furukawa
- Y Furukawa
- Y Shi
- Publication venue
- 'Springer Science and Business Media LLC'
- Publication date
- Field of study