26 research outputs found
Dispositivo per il monitoraggio di sistemi multifune
Dispositivo per il monitoraggio di un sistema multifune dotato di una pluralità di funi di materiale magnetic
Bronchiectasis In Metaphyseal Acroscyphodysplasia With Cone-Shaped Epiphyses (Bellini Disease): A Five Years Follow Up
We present an adolescent with Metaphyseal acroscyphodysplasia (Bellini disease), characterized by severe short stature with accelerated bone maturation, micromelia predominating in the lower limbs, knee flexion, severe brachydactyly, very short hands and feet, metaphyseal changes and specific radiologic features, cup-shaped distal femoral metaphysis with cone-shaped epiphyses, short hands and feet, dental malocclusion. She presented chronic respiratory infections, with secondary bronchiectasis in the course of the follow up.
This is the first case reported in literature of a patient with this extremely rare metaphyseal dysplasia, the Bellini disease, associated with bronchiectasis
The role of attachment patterns and family functioning on psychophysical well-being in children with Cystic Fibrosis Preliminary Results
(1) Introduction
Scientific literature evidences a link between the quality of personal relationships and health status: the attachment style has a role on health and growth outcomes (Feeney, 2000) especially in chronic illness representing a threatening situation (Ciechanowski, 2003). Cystic fibrosis (CF) is a chronic genetic condition compromising the exocrine glands functioning and requiring intensive daily therapies (White et al., 2009). In pediatric condition, infant-mother relationship constituted an important element for nutritional status in CF children (Simmons et al., 1995; Anthony et al. 1999) which is one of the major factors contributing to improve longevity and quality of life.
The study aims to explore attachment patterns of CF children and their mothers, and to examine their relationship with children health status, in terms of quality of eating behaviors and treatment adherence.
(2) Method
At this stage, 29 mothers of CF children (age ranged 4-7 years, M=5,2; SD=1,3) completed Relationship Questionnaire (Bartholomew and Horowitz, 1991) to assess attachment pattern, and Children's Eating Behavior Questionnaire (Wardle et al., 2001) to assess children's eating behaviors. With Separation Anxiety Test (Klagsbrun and Bowlby, 1976) we assessed children's attachment styles. Diet adherence evaluation by FC Centre\u2019s nutritionist, socio-demographic and disease information were recorded and correlated with other outcomes.
(3) Results/discussion
No mother reported Preoccupied attachment pattern and distribution across Secure (N=9), Dismissing (N=11) and Fearful one (N=9) is balanced.
According to the literature on clinical group (Cassiba et al., 2011), we found an high rate of insecure infants (N=20). The most frequent children insecure attachment style is disorganized (N=9) which is mostly linked with maternal dismissing attachment.
Significant correlation between dysfunctional eating behaviors (low food responsiveness and enjoyment, high satiety responsiveness, slowness and fussiness) and compromised health status (low BMI, high hospitalizations number) confirms multidimensionality and dynamicity of pediatric adherence construct (De Civita, Dobkin, 2004). Furthermore, relation between maternal Fearful Attachment and dietary adherence (r=441; p<0,05) confirms how the family functioning plays an important and complex role on the well-being in children with chronic illness (Rolland, 1993) and with CF (Spieth et al., 2001; Zindani et al., 2006)