1 research outputs found
Omental-Mesenteric Myxoid Hamartoma Mimicking Malignancy in a 14-month-old child (A Case Report)
Background: The omental-mesenteric myxoid hamartoma (OMMH) is a very
rare lesion, mainly seen in children and characterized by multiple
omental and mesenteric nodules, which may be confused with malignant
neoplasm. Microscopically, these lesions consist of a richly
vascularized myxoid stroma with plump mesenchymal cells. This lesion
has a benign clinical course without recurrence during follow up. Case
Presentation: We present a 14-month-old boy that was referred with
history of abdominal distension, fever and vomiting for 3 months.
Enhanced computed tomography (CT) revealed a huge well-demarcated
hypodense and spherical mass which displaced bowel loops without
obvious penetration to the intestinal walls.Histological and
immunohistochemical examinations confirmed the diagnosis of OMMH.No
evidence of recurrence was noted during 3 years follow up. Conclusion:
OMMH is a very rare lesion and because of its aggressive appearance,
differential diagnosis with malignancy is warranted. The clinical
picture of our case also led to high suspicion of malignancy. However
by consideration of histological and immunohistochemical findings we
could achieve the correct diagnosis