3 research outputs found
Behçet's disease: a diagnostic challenge in rheumatology. Description of a case series and a review of the literature
9 påginasBehçet disease is a rare autoinflammatory disorder of unknown aetiology and is characterised by systemic manifestations with an exacerbation-remission pattern, often associated with diagnostic delay.
The diagnostic approach to this disease is complex. A report is given on four cases of patients fulfilling the diagnostic criteria for Behçet disease. Other autoimmune rheumatic diseases were considered in the clinical approach. A meticulous clinical evaluation, taking into consideration relapsing aphthous ulcers in oral mucosa and genitalia, and HLA typing allowed a proper diagnosis of Behçet disease to be made.La enfermedad de Behçet es una entidad clĂnica autoinflamatoria, de etiologĂa desconocida, generalmente con compromiso sistĂ©mico, con un patrĂłn de exacerbaciĂłn y remisiĂłn frecuente que se asocia a retraso en el diagnĂłstico.
El diagnĂłstico de esta enfermedad es complejo, por esta razĂłn presentamos 4 casos de pacientes con enfermedad de Behçet, que durante el abordaje clĂnico fueron consideradas otras enfermedades de naturaleza autoinmune. La revisiĂłn integrada de la historia clĂnica, la apariciĂłn de Ășlceras orales y genitales, asĂ como el estudio de tipificaciĂłn del complejo mayor de histocompatibilidad (HLA) permitieron diagnosticar la enfermedad de Behçet