Ascending aortic coarctation - an atypical location in a non-takayasu arteritis female patient

Coarctation of the aorta is a well-known congenital cardiovascular disorder that typically occurs within proximity to the ductus arteriosus. The ascending aorta, distal descending aorta, and abdominal aorta are segments which are prone to development of an atypical coarctation. The etiologies of atypical cases are usually associated with various types of vasculitis syndromes or underlying genetic disorders. In this report, we present a 24-year-old female patient with an ascending aortic coarctation which developed secondary to an atherosclerotic process

Treatment of a patient with congenitally corrected transposition of great arteries associated with ascending aortic hypoplasia and type A interrupted aortic arch without aortic cross clamping leading to myocardial ischemia

İnterrupted aortik ark tedavisi karmaşık bir süreçtir. Cerrahi rekonstrüksiyon genellikle myokard iskemisine neden olan aortik kros klempleme, kalbin durdurulması ve hatta kansız operasyon sahası için derin hipotermi gerektirir.Bu yazıda, normotermik şartlarda, kalbi durdurmadan çıkan aort, aortik ark ve proksimal desendan aort replasmanını selektif kanülasyon ve tüm vücut perfüzyonunu sağlayan cerrahi teknik ile tedavi ettiğimiz konjenital düzeltilmiş büyük arter transpozisyonu, tip A kesintili aortik ark ve hipoplazik asendan aortu olan hastamızı sunuyoruz.Treatment of interrupted aortic arch is complex. Surgical reconstruction consists of procedures that cause myocardial ischemia, such as aortic cross clamping, cardioplegia, and hypothermia. In this article, we present a patient with congenitally corrected transposition of great arteries together with Type A interruption as well as hypoplastic ascending aorta and the aortic arch. The replacement of the aorta, aortic arch, and the proximal descending aorta was performed under normothermic conditions without cardioplegia, which was achieved with a technique that preserves the systemic blood supply by using selective cannulation

Low oxygen saturation following total correction in a patient with tetralogy of fallot and persistant left superior caval vein - How did we diagnose and manage?

Association of tetralogy of Fallot (TOF) with the other intracardiac pathologies such as atrial septal defect (ASD), atrioventricular canal defect or persistent left superior vena cava (PLSVC), absent pulmonary valve are well known pathologies. The associated pathologies require specifi c attention during surgical treatment. In this manuscript, we present management of a four-month-old girl who was diagnosed with TOF and PLSVC but the diagnosis of unroofed coronary sinus was missed in her. Association of unroofed coronary sinus with TOF is a very rare variant of TOF pathology.Souvislost mezi Fallotovou tetralogií (tetralogy of Fallot, TOF) a jinými intrakardiálními patologiemi, jako jsou defekt septa síní (atrial septal defect, ASD), defekt síňokomorového kanálu nebo perzistentní levostranná horní dutá žíla (persistent left superior vena cava, PLSVC) i absence plicní chlopně, je dobře známa. Během chirurgického výkonu vyžadují přidružená onemocnění obzvláštní pozornost. V tomto článku popisujeme léčbu čtyřměsíční dívky s diagnózou TOF a PLSVC, u níž však byl přehlédnut nezastřešený koronární sinus. Nezastřešený koronární sinus se vyskytuje současně s TOF velmi vzácně

Giant aneurysm of non-coronary sinus of valsalva in a patient with marfan sendrom

Valsalva sinüslerinin anevrizmaları, aort anulusu ile sinotubüler bileşke arasındaki aort kök bölgesinin dilatasyonu olarak tanımlanır. Valsalva sinüsünün izole anevrizmaları nadir görülen kardiovasküler patolojilerdir. Sinüs valsalva anevrizması, konjenital veya edinsel kökenli olabilir. Konjenital, özellikle bağ dokusu bozukluklarına sekonder ve konjenital kardiyak defektlerle birlikte görülebilir. Edinsel anevrizmalar ise enfeksiyonlara ve travmaya sekonder olarak oluşabilir. Küçük boyutlu rüptüre olmamış anevrizmalar cerrahi müdahalesiz takip edilebilirken bunun dışındaki tüm hastalarda müdahale gerekir ve cerrahi altın standart tedavi yöntemidir. Bu yazıda, aort yetmezliği ile birlikte non-koroner valsalva sinüsünün dev anevrizması olan ve uygun tedavisi yapılan 12 yaşında Marfan sendromlu hasta anlatılacaktır.Aneurysms of the sinuses of Valsalva are defined as dilatation of the aortic root region be-tween the aortic annulus and the sinotubularjunction. Isolated aneurysms of the sinus of Valsalva are rare cardiovascular pathologies. Sinus valsalva aneurysm may be of congenital or acquired origin. It can occur congenital, secondary to connective tissue disorders or in associa-tion with congenital cardiac defects. Acquired aneurysms may occur secondary to infections and trauma. Small-sized unruptured aneurysms may be followed without surgical treatment; however, surgery may be required in all other patients and surgery is the gold standard treat-ment method. In this article, a 12 -year-old patient with Marfan syndrome who had aortic regurgita-tion and giant aneurysm of the non-coronary sinus of valsalva and was treated appropriately will be presented

Giant pulmonary pseudoaneurysm following balloon dilatation of the pulmonary artery to relieve pulmonary band

Pulmonary artery pseudoaneurysms are uncommon. They may occur secondary to trauma, infectious diseases, vasculitis syndromes, neoplasms, congenital diseases, and pulmonary hypertension. Due to increasing number of cardiac interventions, iatrogenic complications are among the major causes of pulmonary artery pseudoaneurysms.In this report, we present a 6-month-old patient with pulmonary pseudoaneurysm that occurred following pulmonary balloon angioplasty for the relief of a pulmonary band

Congenital tricuspid insufficiency due to rupture of chordae tendinea secondary to intrauterine obliteration of ductus arteriosus

Congenital rupture of tricuspid chordae tendinea leading to severe tricuspid insufficiency is an extremely rare pathology associated with signs and symptoms of congestive heart failure presenting at birth. If the diagnosis and treatment of this pathology are not made early in life fetal demise may become inevitable. We herein present a neonate with central cyanosis and congestive heart failure due to rupture of an anterior leaflet chordae resulting in severe insufficiency of the tricuspid valve who was treated with appropriate surgery