Abnormal Metabolism of γ-Trace Alkaline Microprotein : The Basic Defect in Hereditary Cerebral Hemorrhage with Amyloidosis

ALTHOUGH the total incidence of cerebral hemorrhage is high, comparatively few reports concerning the familial occurrence of this disease have been published.1,2 In 1935 Arnason described 10 families with a high incidence of cerebral hemorrhage and concluded that a hereditary form of the disease was present in these families.3 Further clinicopathological investigations of the disease revealed an autosomal dominant inheritance and a connection between the disease and a special form of amyloidosis confined to the cerebral vasculature.4 This type of cerebral hemorrhage is therefore generally referred to as hereditary cerebral hemorrhage with amyloidosis. Recently, the fibrillar components of the amyloid

Remembering the Dead: Agency, Authority, and Mortuary Practices in Interreligious Families in the United States

This chapter asks how cultural rules for treatment of the body and spirit of the deceased and for memorialization are adapted in mortuary ritual in a pluralistic society. Social and technological changes in the United States have challenged customary religious practices in which the nature of the dead and the authority of the clergy were established. New ideologies give increased agency to the deceased to express individual preferences. That agency extends to the expectation that as moral obligation to the deceased, family and friends will represent after death who the person was in life. The expression of ethics to honor the dead may be accomplished through modifications of ritual practice and the use of new technologies that democratize the sociocultural process of creating the meaning and memory of the deceased person