Skip to main content
Article thumbnail
Location of Repository

Generalized Lymphangiomatosis: Radiologic Findings in Three Pediatric Patients

By Dong Hyun Yang and Hyun Woo Goo

Abstract

Generalized lymphangiomatosis is a rare disease that is characterized by widespread bony and soft tissue involvement of lymphangioma. Radiological evaluation is crucial because the site and extent of the lymphangioma are important prognostic factors. We reported here on three cases of generalized lymphangiomatosis and all three cases showed similar radiologic findings, but a different clinical course. The CT, US and MR images showed sharply defined, non-enhanced cystic lesions involving the mediastinum, bones, spleen, lung and lower neck. The whole body MR imaging with the short tau inversion recovery (STIR) sequence showed good capability for evaluating the extent of disease

Topics: Case Report
Publisher: The Korean Radiological Society
OAI identifier: oai:pubmedcentral.nih.gov:2667616
Provided by: PubMed Central
Download PDF:
Sorry, we are unable to provide the full text but you may find it at the following location(s):
  • http://www.pubmedcentral.nih.g... (external link)
  • Suggested articles

    Citations

    1. Cervical lymphangiomatosis with progressive craniospinal deformity.
    2. CT and MR imaging of generalized cystic lymphangiomatosis in pediatric patients.
    3. (1996). Cystic angiomatosis: case report and review of the literature. Skeletal Radiol
    4. Cystic lymphangioma in children: report of 32 children including lesions at rare sites.
    5. (1998). Diffuse neonatal gastrointestinal hemangiomatosis: CT findings. Pediatr Radiol
    6. (1992). Generalized lymphangiomatosis and chylothorax in the pediatric age group. Pediatr Pulmonol
    7. Langerhans’ cell histiocytosis: pathology, imaging and treatment of skeletal involvement.
    8. (2006). Treatment of thoracic lymphangiomatosis.
    9. Whole-body magnetic resonance imaging: a useful additional sequence in paediatric imaging.

    To submit an update or takedown request for this paper, please submit an Update/Correction/Removal Request.