Since the association of syringomyelia and neurofibromatosis is mostly related to intramedullary tumors, syringomyelia in neurofibromatosis type 1 (NF-1) is much rarer than in neurofibromatosis type 2 (NF-2). In this paper, we present a case of NF-1 associated with an idiopathic syringomyelia extending from conus medullaris to the upper pens and discuss the relationship between neurofibromatosis and syringomyelia
