6 research outputs found
Subependymome du ventricule lateral: presentation dâune serie de 5 cas et revue de la litterature.
Description Les subĂ©pendymomes sont des tumeurs bĂ©nignes rares, de dĂ©couverte souvent fortuite et siĂ©geant prĂ©fĂ©rentiellement au niveau du quatriĂšme ventricule, plus rarement au niveau du ventricule latĂ©ral.Objectif Le but de notre Ă©tude est de prĂ©senter notre expĂ©rience en matiĂšre de subĂ©pendymomes du ventricule latĂ©ral et de discuter leurs caractĂ©ristiques cliniques, radiologiques, de prise en charge et pronostiques au vu des donnĂ©es actuelles de la littĂ©rature.MĂ©thode Etude rĂ©trospective de cinq cas de subĂ©pendymomes symptomatiques du ventricule latĂ©ral pris en charge au sein de notre institution au cours des dix derniĂšres annĂ©es.RĂ©sultats Cinq sujets de sexe masculin avec des subĂ©pendymomes histologiquement prouvĂ©s ont Ă©tĂ© recensĂ©s. LâĂąge moyen Ă©tait de 35.2 ans. La prĂ©sentation clinique allait du dĂ©but brutal avec aggravation rapide de lâĂ©tat neurologique aux formes insidieuses avec syndrome dâhypertension intracrĂąnienne Ă©voluant depuis un an. La tumeur Ă©tait confinĂ©e au ventricule latĂ©ral dans trois cas et Ă©tendue au troisiĂšme ventricule dans les deux autres cas avec une taille allant de 12 Ă 42 mm. LâexĂ©rĂšse complĂšte par un abord trans calleux Ă©tait rĂ©alisĂ©e dans tous les cas. LâĂ©volution Ă©tait favorable avec absence de rĂ©cidive aprĂšs un suivi moyen de 6 ans 2 mois.Conclusion Les subĂ©pendymomes du ventricule latĂ©ral sont rares, avec une symptomatologie variable et une Ă©volution imprĂ©visible. La chirurgie est la modalitĂ© thĂ©rapeutique de choix et lâexĂ©rĂšse totale doit ĂȘtre envisagĂ©e dans tous les cas.Mots clĂ©s : Chirurgie, Imagerie par rĂ©sonance magnĂ©tique, SubĂ©pendymome, Ventricule latĂ©ral, SubĂ©pendymome, Ventricule latĂ©ra
Osteolytic clear cell meningioma of the petrous bone occurring 36 years after posterior cranial fossa irradiation: Case report
Objective and importance
While bone invasion and hyperostosis are frequent phenomena in meningiomas, primary intraosseous meningiomas are rare and their occurrence in the skull base is an extraordinary exception. Moreover, radiation-induced meningiomas represent a unique clinical dilemma given the fact that patients with these tumors had often received a prior full course of radiotherapy.
Clinical presentation
A 42-year-old man presented with a 3-month history of progressively worsening facial asymmetry. His medical history was consistent for a posterior cranial fossa irradiation at the age of 6 years for a non-confirmed brain stem tumor. On admission his Karnofsky performance status was graded as 50% and his neurological examination showed a complete right facial nerve paralysis and hearing impairment. Computed tomography and magnetic resonance imaging demonstrated an osteolytic tumor invading the whole right petrous bone without intracranial involvement.
Intervention
As the tumor reached the external auditory canal, a tissue sample was obtained locally. Pathological examination of the lesion identified a grade II clear cell meningioma and the patient was consequently addressed for an intensity modulated radiation therapy. His condition remained unchanged till the most recent follow-up examination, 8 months later.
Conclusions
To the best of our knowledge, a radiation induced osteolytic clear cell meningioma of the petrous bone has not been previously reported. As little literature exists regarding the use of adjuvant therapies for these tumors, intensity modulated radiation therapy remains an attractive treatment option in case of pervious irradiation and general status alteration
Cerebellar liponeurocytoma with extracranial extension: Case report
Cerebellar liponeurocytoma is a newly recognized, rare clinicopathological entity commonly described in the cerebellar hemispheres or the vermis.
We present a rare case of cerebellar liponeurocytoma arising from the left cerebellar amygdala with extracranial extension. Such a condition has never been previously reported
Multiple spinal metastases from a well-differentiated liposarcoma of the iliac wing: a case report
Liposarcoma (LPS) is an uncommon connective tissue tumor arising from lipoblast cells. Well-differentiated liposarcoma (WDLPS) represents the most frequent subtype. It mostly occurs in the limbs or retroperitoneum of elderly individuals and typically has no propensity to metastasize, unless it undergoes dedifferentiatio
Cavernous Hemangioma of the Skull and Meningioma: Association or Coincidence?
Intraosseous cavernous hemangiomas of the skull are rare. Meningiomas are quite frequently encountered in a neurosurgical practice. The association between these two entities is nevertheless very uncommon. The authors present a case of a 72-year-old woman suffering from headache. The MRI showed a parietal meningioma with adjacent thick bone. The meningioma and the bone were removed. The histological examination confirmed the diagnosis of meningioma and revealed a cavernoma of the skull. The relationship between the lesions suggests more than a coincidental association. Several hypotheses are proposed to explain common causal connections