Subependymome du ventricule lateral: presentation d’une serie de 5 cas et revue de la litterature.

Description Les subépendymomes sont des tumeurs bénignes rares, de découverte souvent fortuite et siégeant préférentiellement au niveau du quatrième ventricule, plus rarement au niveau du ventricule latéral.Objectif Le but de notre étude est de présenter notre expérience en matière de subépendymomes du ventricule latéral et de discuter leurs caractéristiques cliniques, radiologiques, de prise en charge et pronostiques au vu des données actuelles de la littérature.Méthode Etude rétrospective de cinq cas de subépendymomes symptomatiques du ventricule latéral pris en charge au sein de notre institution au cours des dix dernières années.Résultats Cinq sujets de sexe masculin avec des subépendymomes histologiquement prouvés ont été recensés. L’âge moyen était de 35.2 ans. La présentation clinique allait du début brutal avec aggravation rapide de l’état neurologique aux formes insidieuses avec syndrome d’hypertension intracrânienne évoluant depuis un an. La tumeur était confinée au ventricule latéral dans trois cas et étendue au troisième ventricule dans les deux autres cas avec une taille allant de 12 à 42 mm. L’exérèse complète par un abord trans calleux était réalisée dans tous les cas. L’évolution était favorable avec absence de récidive après un suivi moyen de 6 ans 2 mois.Conclusion Les subépendymomes du ventricule latéral sont rares, avec une symptomatologie variable et une évolution imprévisible. La chirurgie est la modalité thérapeutique de choix et l’exérèse totale doit être envisagée dans tous les cas.Mots clés : Chirurgie, Imagerie par résonance magnétique, Subépendymome, Ventricule latéral, Subépendymome, Ventricule latéra

Osteolytic clear cell meningioma of the petrous bone occurring 36 years after posterior cranial fossa irradiation: Case report

Objective and importance While bone invasion and hyperostosis are frequent phenomena in meningiomas, primary intraosseous meningiomas are rare and their occurrence in the skull base is an extraordinary exception. Moreover, radiation-induced meningiomas represent a unique clinical dilemma given the fact that patients with these tumors had often received a prior full course of radiotherapy. Clinical presentation A 42-year-old man presented with a 3-month history of progressively worsening facial asymmetry. His medical history was consistent for a posterior cranial fossa irradiation at the age of 6 years for a non-confirmed brain stem tumor. On admission his Karnofsky performance status was graded as 50% and his neurological examination showed a complete right facial nerve paralysis and hearing impairment. Computed tomography and magnetic resonance imaging demonstrated an osteolytic tumor invading the whole right petrous bone without intracranial involvement. Intervention As the tumor reached the external auditory canal, a tissue sample was obtained locally. Pathological examination of the lesion identified a grade II clear cell meningioma and the patient was consequently addressed for an intensity modulated radiation therapy. His condition remained unchanged till the most recent follow-up examination, 8 months later. Conclusions To the best of our knowledge, a radiation induced osteolytic clear cell meningioma of the petrous bone has not been previously reported. As little literature exists regarding the use of adjuvant therapies for these tumors, intensity modulated radiation therapy remains an attractive treatment option in case of pervious irradiation and general status alteration

Cerebellar liponeurocytoma with extracranial extension: Case report

Cerebellar liponeurocytoma is a newly recognized, rare clinicopathological entity commonly described in the cerebellar hemispheres or the vermis. We present a rare case of cerebellar liponeurocytoma arising from the left cerebellar amygdala with extracranial extension. Such a condition has never been previously reported

Multiple spinal metastases from a well-differentiated liposarcoma of the iliac wing: a case report

Liposarcoma (LPS) is an uncommon connective tissue tumor arising from lipoblast cells. Well-differentiated liposarcoma (WDLPS) represents the most frequent subtype. It mostly occurs in the limbs or retroperitoneum of elderly individuals and typically has no propensity to metastasize, unless it undergoes dedifferentiatio

Cavernous Hemangioma of the Skull and Meningioma: Association or Coincidence?

Intraosseous cavernous hemangiomas of the skull are rare. Meningiomas are quite frequently encountered in a neurosurgical practice. The association between these two entities is nevertheless very uncommon. The authors present a case of a 72-year-old woman suffering from headache. The MRI showed a parietal meningioma with adjacent thick bone. The meningioma and the bone were removed. The histological examination confirmed the diagnosis of meningioma and revealed a cavernoma of the skull. The relationship between the lesions suggests more than a coincidental association. Several hypotheses are proposed to explain common causal connections