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A Rare Case of Pulmonary Artery Sling with the VACTERL Association in a 20-Month-Old Infant

By Yazdan Ghandi, Akbar Shafiee, , Mehrazad Sharifi and Najmeh Sadat Bolandnazar


<p><em>The VACTERL association, co-occurrence of vertebral, anorectal, cardiac, tracheoesophageal, genitourinary, and limb malformations, is a rare congenital anomaly. Several cardiac anomalies have been reported as a part of the VACTERL association, particularly ventricular and atrial septal defects. Pulmonary artery sling is a rare congenital abnormality in which the left pulmonary artery arises from the right pulmonary artery. This anomaly is not frequently observed in the VACTERL association and has been rarely reported.  A 20-month-old girl was admitted to our hospital due to pneumonia in the right lung, which had pulmonary artery sling as a part of the VACTERL association. Barium meal X-ray showed pressure effects on the esophagus, and computed tomography angiography revealed pulmonary artery sling. Pneumonia management was done. However, the parents of our patient refused to give consent for the surgical correction of this vascular anomaly. Three months after discharge from the hospital, the patient was visited, at which time the parents again refused surgery and treatment for their daughter despite our recommendations.</em> <em></em></p

Topics: Congenital abnormalities • Heart defects, congenital • Pulmonary artery • VACTERL association, Diseases of the circulatory (Cardiovascular) system, RC666-701
Publisher: Tehran University of Medical Sciences
Year: 2017
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