Article thumbnail

A Case of Myxoid Dermatofibrosarcoma Protuberans

By Yeon Ju Hong, You Won Choi, Ki Bum Myung and Hae Young Choi


Dermatofibrosarcoma protuberans (DFSP) is a slowly growing dermal spindle cell tumor and its myxoid variant, a rare type of DFSP, is characterized by extensive myxoid degeneration. We present the case of a 69-year-old woman with a multinodular reddish plaque on her trunk. Histopathologically, the tumor was located in the dermis and consisted of uniform spindle-shaped cells, showing strongly positive reaction for CD34, and negative for both S-100 and desmin. In addition to the typical storiform pattern, prominent myxoid stromal changes were demonstrated. Herein, we report an interesting case of myxoid DFSP, rarely reported in the dermatology literature

Topics: Case Report
Publisher: Korean Dermatological Association; The Korean Society for Investigative Dermatology
OAI identifier:
Provided by: PubMed Central

To submit an update or takedown request for this paper, please submit an Update/Correction/Removal Request.

Suggested articles


  1. Clinicopathologic and molecular genetic characterization of low-grade fibromyxoid sarcoma, and cloning of a novel FUS/CREB3L1 fusion gene.
  2. (1997). Immunohistochemical characterization of dermatofibrosarcoma protuberans with practical applications for diagnosis and treatment.
  3. Myxoid dermatofibrosarcoma protuberans: a rare variant analyzed in a series of 23 cases.
  4. Myxoid dermatofibrosarcoma protuberans: clinicopathologic, immunohistochemical, and molecular analysis of eight cases.
  5. Myxoid tumours of soft tissue.
  6. (2005). Pathology of the skin: with clinical correlations. Vol 2.