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Undifferentiated connective tissue disease presenting with prevalent interstitial lung disease: Case report and review of literature

By Francesca Lunardi, Elisabetta Balestro, Beatrice Nordio, Franco Cozzi, Roberta Polverosi, Paolo Sfriso, Fausto Braccioni and Fiorella Calabrese


Undifferentiated connective tissue diseases (UCTDs) are clinical entities characterised by signs and symptoms suggestive of a systemic autoimmune disease, which do not fulfil the diagnostic criteria for a defined connective tissue disease. Lung involvement can complicate the course and management of the disease, often determining a worse outcome. Respiratory dysfunction as the first clinical manifestation has seldom been reported

Topics: Case Report
Publisher: BioMed Central
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Provided by: PubMed Central

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