Article thumbnail

Omphalocele and alveolar capillary dysplasia: a new association.

By L.C. Gerrits, A.C. de Mol, J. Bulten, F.H.J.M. van der Staak and A.F.J. van Heijst

Abstract

OBJECTIVE: First report of an infant with coexistent omphalocele and alveolar capillary dysplasia. DESIGN: Descriptive case report. SETTING: Neonatal intensive care unit of a tertiary care children's hospital. PATIENT: We describe a term infant with omphalocele and respiratory insufficiency attributable to pulmonary hypertension. The patient was placed on extracorporeal membrane oxygenation, but the pulmonary hypertension persisted. After 10 days on extracorporeal membrane oxygenation, a lung biopsy was performed. It showed alveolar capillary dysplasia. Because of the lethal prognosis, extracorporeal membrane oxygenation was withdrawn and the patient expired. CONCLUSIONS: This is the first description of an association between omphalocele and alveolar capillary dysplasia. In newborns with omphalocele who have severe respiratory insufficiency and pulmonary hypertension, alveolar capillary dysplasia should be considered

Year: 2010
DOI identifier: 10.1097/pcc.0b013e3181b80a75
OAI identifier:
Provided by: NARCIS
Download PDF:
Sorry, we are unable to provide the full text but you may find it at the following location(s):
  • http://www.loc.gov/mods/v3 (external link)
  • http://hdl.handle.net/2066/872... (external link)
  • http://hdl.handle.net/2066/872... (external link)
  • https://repository.ubn.ru.nl/b... (external link)
  • https://repository.ubn.ru.nl/d... (external link)
  • Suggested articles


    To submit an update or takedown request for this paper, please submit an Update/Correction/Removal Request.