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Isolated Ventricular Noncompaction Syndrome in a Nigerian Male: Case Report and Review of the Literature

By Indrani S. Bhattacharya, Marc Dweck, Andrew Gardner, Mark Jones and Mark Francis


Isolated ventricular non-compaction cardiomyopathy (IVNC) is a rare, morphologically distinct primary genetic cardiomyopathy, which is now gaining prominence as an important differential diagnosis in patients presenting with cardiac failure. We describe a case report of a Nigerian male with facial dysmorphism presenting with cardiac failure. This is followed by a review of the literature with focus on the diagnosis of this condition, which may be difficult especially in non-Caucasian populations

Topics: Case Report
Publisher: SAGE-Hindawi Access to Research
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Provided by: PubMed Central

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