Status dystonicus (aka Dystonic storm) is defined as a movement disorder emergency in which there is pro-longed, generalised, intense and painful muscle con-traction. Up to 60 % of the reported cases are children,1 but the true incidence is unknown. SD is probably under recognised and can be fatal in up to 10 % of cases.1 Patients at risk are those with chronic dystonias (primary and secondary), quadriplegic cere-bral palsy, neurodegenerative disorders, post acquired brain injury and acute drug withdrawal (especially baclofen). Common triggers are pain, infection, surgery and drugs. Main differentiating features of SD are hypertonia, abnormal dystonic postures, preservation of conscious-ness and hyperCKaemia. Non-convulsive status epilep
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