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Gerstmann-Sträussler-Scheinker disease subtypes efficiently transmit in bank voles as genuine prion diseases.

By Laura Pirisinu, Michele A. Di Bari, Claudia D’Agostino, Stefano Marcon, Geraldina Riccardi, Anna Poleggi, Mark L. Cohen, Brian S. Appleby, Pierluigi Gambetti, Bernardino Ghetti, Umberto Agrimi and Romolo Nonno

Abstract

Gerstmann-Sträussler-Scheinker disease (GSS) is an inherited neurodegenerative disorder associated with mutations in the prion protein gene and accumulation of misfolded PrP with protease-resistant fragments (PrPres) of 6–8 kDa

Topics: Gerstmann-Sträussler-Scheinker disease, neurodegenerative disorders, 6-8 kDa
Publisher: 'Springer Science and Business Media LLC'
Year: 2016
DOI identifier: 10.1038/srep20443
OAI identifier: oai:scholarworks.iupui.edu:1805/9112
Provided by: IUPUIScholarWorks
Journal:

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