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Congenital heart block associated with Sjögren syndrome: case report

By Karwan A. Moutasim, Penelope J. Shirlaw, Michael P. Escudier and Timothy W.J. Poate


Background: Congenital heart block is a rare complication of pregnancy associated with Sjögren Syndrome that may result in the death of the foetus or infant, or the need for pacing in the newborn or at a later stage.<br/><br/>Case report: The case is presented of a 64-year-old patient with primary Sjögren Syndrome and a history of having given birth to two sons with congenital heart block, both of whom required pacing several years later.<br/><br/>Conclusion: The literature relating to this association is discussed including the suggested mechanism, long-term outcome of mothers of children with congenital heart block and preventive treatment strategies

Topics: RB, RG, QH426
Year: 2009
OAI identifier: oai:eprints.soton.ac.uk:165295
Provided by: e-Prints Soton

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