Dental Management of a Young Child Affected by Galactosialidosis and a Gigantic Abdominal Growth

Abstract

Galactosialidosis (GS) is a rare form of lysosomal storage disease that involves a broad spectrum of skeletal and soft tissue abnormalities. We report here on a 4-year 7-month-old boy with mild mental retardation, exhibiting multiple caries cavities and associated infectious foci and macroglossia. A huge abdominal enlargement due to peritoneal ascites was evident. Behavioral management and patient positioning on the dental chair represented a true challenge. The patient was treated under general anesthesia. However, life-threatening postoperative complications occurred because of the impossibility of extubating the patient. A very careful preanesthetic assessment is crucial in children affected by general conditions associated with airway anomalies, such as GS

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https://doaj.org/toc/2090-6455 (external link)

https://doaj.org/toc/2090-6447 (external link)

http://dx.doi.org/10.1155/2018... (external link)

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