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Dental Management of a Young Child Affected by Galactosialidosis and a Gigantic Abdominal Growth

By Yoselín Méndez-Salado, Paola De Ávila-Rojas, Amaury Pozos-Guillén, Raúl Márquez-Preciado, Miguel Ángel Noyola-Frías, Socorro Ruiz-Rodríguez and Arturo Garrocho-Rangel

Abstract

Galactosialidosis (GS) is a rare form of lysosomal storage disease that involves a broad spectrum of skeletal and soft tissue abnormalities. We report here on a 4-year 7-month-old boy with mild mental retardation, exhibiting multiple caries cavities and associated infectious foci and macroglossia. A huge abdominal enlargement due to peritoneal ascites was evident. Behavioral management and patient positioning on the dental chair represented a true challenge. The patient was treated under general anesthesia. However, life-threatening postoperative complications occurred because of the impossibility of extubating the patient. A very careful preanesthetic assessment is crucial in children affected by general conditions associated with airway anomalies, such as GS

Topics: Dentistry, RK1-715
Publisher: Hindawi Limited
Year: 2018
DOI identifier: 10.1155/2018/2086157
OAI identifier: oai:doaj.org/article:e6cbae01122a4c7f96a246d60dd05b44
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