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Doença cística medular do rim: relato de um caso diagnosticado por ultra-sonografia e tomografia computadorizada Medullary cystic disease of the kidney: report of a case diagnosed by ultrasonography and computed tomography examinations

By Tarcísio Nunes Carvalho, Cyrillo Rodrigues de Araújo Jr., Sérgio Roberto Fraguas Filho, Marlos Augusto Bittencourt Costa, Flávia Aparecida de Souza Ribeiro and Kim-Ir-Sen Santos Teixeira

Abstract

Doença cística medular, nefronofitíase juvenil familiar ou complexo de doença cística medular referem-se a um grupo de doenças similares cuja lesão básica é uma progressiva atrofia tubular renal com esclerose glomerular e formação cística medular. É importante causa de insuficiência renal em pacientes adolescentes. Estudos de imagem têm papel principal no diagnóstico desta enfermidade, com cistos caracteristicamente individualizados na medula renal e junção córtico-medular e tamanho renal normal ou reduzido. Neste artigo demonstramos os achados de imagem da doença cística medular renal em uma adolescente com quadro clínico característico, por meio de ultra-sonografia e tomografia computadorizada.<br>The terms medullary cystic disease, juvenile nephronophthisis or medullary cystic disease complex refer to a group of similar diseases in which the basic pathological abnormality is progressive renal tubular atrophy with secondary glomerular sclerosis and medullary cystic formation. Medullary cystic disease is an important cause of renal failure in adolescent patients. Imaging methods play a primary role in the diagnosis of these diseases. Cysts are characteristically seen in the renal medulla and corticomedullary junction whereas kidneys may be of normal to small size. In this article we present the ultrasonography and computed tomography findings of a female adolescent patient with characteristic clinical picture of medullary cystic disease

Topics: Nefronofitíase juvenil familiar, Ultra-sonografia, Tomografia computadorizada, Familial juvenile nephronophthisis, Ultrasonography, Computed tomography, Medical physics. Medical radiology. Nuclear medicine, R895-920, Medicine (General), R5-920, Medicine, R, DOAJ:Internal medicine, DOAJ:Medicine (General), DOAJ:Health Sciences
Publisher: Colégio Brasileiro de Radiologia e Diagnóstico por Imagem
Year: 2003
DOI identifier: 10.1590/S0100-39842003000600013
OAI identifier: oai:doaj.org/article:486b1f65c03f4d0199ae600f11512179
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